Table 2

Case 1. Biochemical data on first presentation in 1980: 24 urine steroid studies

Cortisol derivatives (mmol/mol creatinine) Cortisol precursors (mmol/mol creatinine)
Baseline23.590.75
Low dose dexamethasone 0.5 mg 6 hourlyBasal 14.15Basal 4.27
After 9.31After 0.75
High dose dexamethasone 2 mg 6 hourlyBasal 5.08Basal 0.45
After 4.00After 0.27
On metyraponeBasal 6.26Basal 35.36
After 15.3After 65.97