Table 1

Characteristics of the two main variants

Diffuse (%) Limited (%)
Cutaneous sclerosisProximalDistal (hands, feet,  face, forearms)
Raynaud's phenomenonRecentOld (for years)
Calcinosis2040
Telangiectasia6090
Interstitial pulmonary fibrosis705
Pulmonary hypertension535
Renal crisis201
Anti Scl-70 antibodies3010
Anticentromere antibodies1075
Ten years' survival5070