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Primary hepatic perivascular epithelioid cell neoplasm (PEComa) with fever in a 53-year-old man
  1. Gang Xu,
  2. Haifeng Xu,
  3. Huayu Yang,
  4. Shunda Du,
  5. Yilei Mao
  1. Liver Surgery, Peking Union Medical College Hospital, Chinese Academy of Medical Science and Peking Union Medical College, Beijing, China
  1. Correspondence to Professor Yilei Mao, Liver Surgery, Peking Union Medical College Hospital, Beijing 100730, China; pumch-liver{at}

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A 53-year-old male patient, presenting merely with fever for a week, was admitted to the hospital. Contrast-enhanced CT showed a round inhomogeneous enhancement lesion on the early arterial phase and washout in the portal phase (figure 1A,B). Hepatitis virus tests and tumour markers in serum were all negative. Considering the atypical imaging features of intrahepatic space-occupying lesions, the possibility of liver tumours or liver abscesses is not excluded. The patient underwent combined multisegmental hepatectomy. Postoperative pathology revealed hepatic perivascular epithelioid cell neoplasm (PEComa) (figure 2A). The pathological result revealed positive immunostaining for melanocytic markers (HMB-45), Melan-A and …

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  • Contributors GX wrote the first draft of the manuscript and submitted the manuscript. HX and HY were in charge of the patient and collected the clinical data. SD and YM critically revised the manuscript. All authors approved the final version.

  • Funding This study was funded by CAMS Innovation Fund for Medical Sciences (CIFMS) (No. 2016-I2M-1-001) and the National High-tech Research and Development Projects (863) (No. 2015AA020303).

  • Competing interests None declared.

  • Patient consent for publication Not required.

  • Provenance and peer review Not commissioned; externally peer reviewed.