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IgG4-related disease: a new entity sometimes needs a retrospective diagnosis
  1. Maristela Böhlke1,
  2. Gabriel Santos2
  1. 1Dialysis and Kidney Transplantation Department, Hospital Universitário São Francisco de Paula, and Health and Behavior Postgraduate Program, Universidade Católica de Pelotas, Pelotas, Brasil
  2. 2Pathology Department, Santa Casa de Misericórida de Porto Alegre, Porto Alegre, Brasil
  1. Correspondence to Professor Maristela Böhlke, Rua Canoas 1054, Pelotas CEP 96090130, Brasil; mbohlke.sul{at}

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A 60-year-old male patient presented with a 4-year history of retroperitoneal fibrosis (RF) compressing the aorta, inferior vena cava, left renal vein and left ureter, with ipsilateral renal atrophy. At the time of RF diagnosis, positron emission tomography (PET) scan had shown an expansive retroperitoneal lesion involving large vessels (figure 1). He had also presented a high C-reactive protein (CRP), reduced glomerular filtration rate, polyclonal peak in serum gamma globulins and retroperitoneal biopsy had …

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