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Postgrad Med J 89:305-306 doi:10.1136/postgradmedj-2012-131469
  • Images in medicine

Anomalous pulmonary venous drainage: chest radiography and cardiac imaging

  1. Nikolaos Tzemos3
  1. 1Department of Cardiology, Regional Cardiac-Cardiothoracic Centre, University Hospital Morriston, Swansea, UK
  2. 2Department of Cardiology, Ninewells Hospital and Medical School, Dundee, UK
  3. 3Institute of Cardiovascular and Medical Sciences, University of Glasgow, Glasgow, UK
  1. Correspondence to Dr Pandula Athauda-arachchi, Department of Cardiology, Regional Cardiac-Cardiothoracic Centre, University Hospital Morriston, Swansea, SA6 6LN, UK; pma29{at}cantab.net

Introduction

Scimitar syndrome (or pulmonary veno-lobar syndrome) is a rare congenital cardiac condition characterised by abnormal pulmonary venous return from the right lung directly into the inferior vena cava. It can be associated with hypoplastic right lung, pulmonary artery hypoplasia and dextrocardia, among others.1 ,2 There are complete and incomplete variations. In the complete form, classically, the right lung is hypoplastic and is supplied by a systemic arterial branch from the aorta with hypoplasia of the right pulmonary artery, resulting in an abnormal right heart border on imaging.

Most cases are diagnosed …