Acquired haemophilia is rare and potentially fatal, with a mortality of 20% if left untreated. There is a strong association with other autoimmune diseases. This report describes a patient with rheumatoid arthritis, vitiligo, and bullous pemphigoid where the diagnosis of acquired haemophilia was made after an extensive bleed into a bullous lesion in the buccal mucosa. This case highlights some of the potential complications of acquired haemophilia and its treatment.
- acquired haemophilia
- bullous pemphigoid
- buccal haematoma
- factor VIII inhibitor concentration
- factor eight inhibitor bypassing activity (FEIBA)