Article Text


Primary shunt hyperbilirubinaemia: a variant of the congenital dyserythropoietic anaemias.
  1. A. R. Bird,
  2. E. Knottenbelt,
  3. P. Jacobs,
  4. J. Maigrot
  1. University of Cape Town Leukaemia Centre, South Africa.


    A 19 year old Mauritian male presented with episodic nausea, abdominal discomfort and jaundice. Unconjugated hyperbilirubinaemia and erythroid hyperplasia without dyserythropoiesis led to the diagnosis of primary shunt hyperbilirubinaemia. The similarity between congenital dyserythropoietic anaemia and this entity suggests that patients with these lesions can be considered within a single spectrum of disorders, characterized as congenital ineffective erythropoiesis.

    Statistics from

    Request permissions

    If you wish to reuse any or all of this article please use the link below which will take you to the Copyright Clearance Center’s RightsLink service. You will be able to get a quick price and instant permission to reuse the content in many different ways.